ISSN: 2149-2247 | E-ISSN: 2149-2549
Volume : 43 Issue : 4 Year : 2021
Celiac Disease and Autoimmune Hepatitis Presenting with Fulminant Hepatic Failure: A Case Report [Erciyes Med J]
Erciyes Med J. 2021; 43(4): 403-405 | DOI: 10.14744/etd.2020.21456

Celiac Disease and Autoimmune Hepatitis Presenting with Fulminant Hepatic Failure: A Case Report

Kadriye Nil Kaptan, Taner Özgür, Enes Turan, Tanju Özkan
Department of Pediatric Gastroenterology, Bursa Uludağ University Faculty of Medicine, Bursa, Turkey

Background: Fulminant hepatic failure (FHF) may be a rare presentation of autoimmune hepatitis (AIH) in previously asymptomatic adolescents. Celiac disease (CD) is a chronic immune disease that may be associated with severe forms of liver disease and coexists with AIH. We report a patient presenting with an FHF at the diagnosis of AIH and CD.
Case Report: An 8-year-old female patient who had no known background or family history of liver disease was referred to our center with an FHF diagnosis. Her clinical and laboratory findings fulfilled the criteria of seronegative AIH and CD. After 7 days of starting the medical treatment, encephalopathy and liver function tests gradually improved.
Conclusion: AIH and CD usually follow a chronic course and rarely coexist. However, they should be considered the etiologies of FHF and should be treated promptly.

Keywords: Autoimmune hepatitis, celiac disease, children, fulminant hepatic failure.

Kadriye Nil Kaptan, Taner Özgür, Enes Turan, Tanju Özkan. Celiac Disease and Autoimmune Hepatitis Presenting with Fulminant Hepatic Failure: A Case Report. Erciyes Med J. 2021; 43(4): 403-405

Corresponding Author: Kadriye Nil Kaptan, Türkiye
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